Litcius/Paper detail

Mycophenolate Mofetil for Eosinophilic Fasciitis

Elizabeth Tkachenko, Alexa B. Steuer, Kelly Lo, Avery LaChance, Joseph F. Merola, Alisa N. Femia, Ruth Ann Vleugels

2020JAMA Dermatology15 citationsDOIOpen Access PDF

Abstract

Eosinophilic fasciitis (EF) is a fibrosing disorder characterized by edema, erythema, and induration of the extremities. Eosinophilic fasciitis can cause substantial morbidity from joint contractures, and permanent fibrosis may ensue without timely treatment. 1 Corticosteroids are considered firstline therapy; however, long-term treatment with corticosteroidsparing agents is required to avoid sequelae of chronic steroid use and achieve a durable clinical response. Although methotrexate is often considered the first-line corticosteroidsparing agent for EF, there is no standardized treatment ladder. To our knowledge, 3 cases of EF have reported favorable outcomes with mycophenolate mofetil (MMF) to date. Given the paucity of data, we investigated the clinical response of EF to MMF in 3 tertiary care centers.

Topics & Concepts

MedicineMycophenolateEosinophilic fasciitisDermatologyFasciitisEosinophilic esophagitisMycophenolic acidPathologyInternal medicineSurgeryDiseaseTransplantationEosinophilic Disorders and SyndromesEosinophilic EsophagitisInterstitial Lung Diseases and Idiopathic Pulmonary Fibrosis