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UQCRC2-related mitochondrial complex III deficiency, about 7 patients

Claire Bansept, Pauline Gaignard, Élise Lebigot, Didier Eyer, Geoffroy Delplancq, Célia Hoebeke, K. Mazodier, Anaïs Ledoyen, Cécile Rouzier, Konstantina Fragaki, Samira Ait‐El‐Mkadem Saadi, Christophe Philippe, Ange‐Line Bruel, Laurence Faivre, François Feillet, Marie‐Thérèse Abi Wardé

2022Mitochondrion15 citationsDOI

Topics & Concepts

Coenzyme Q10Lactic acidosisCoenzyme Q – cytochrome c reductaseMitochondrial diseaseUbiquinolMitochondrionPhenotypeGeneReductasePoint mutationBiologyMedicineBiochemistryCytochrome cChemistryGeneticsMitochondrial DNAEnzymeMutationMitochondrial Function and PathologyMetabolism and Genetic DisordersCoenzyme Q10 studies and effects
UQCRC2-related mitochondrial complex III deficiency, about 7 patients | Litcius