IgG4-related disease—rare but you should not forget it
Frederico Augusto Gurgel Pinheiro, Ivânio Alves Pereira, Alexandre Wagner Silva de Souza, Henrique Ayres Mayrink Giardini, Rafael Alves Cordeiro
Abstract
Immunoglobulin G4-related disease is a systemic immune-mediated disease with insidious evolution characterized by fibroinflammatory lesions over virtually any organ system. Despite the remarkable progression of knowledge, its etiology remains undefined. Due to its relapse-remitting pattern, it could accumulate irreversible damage, increasing comorbidities and mortality. This paper emphasizes key concepts for diagnosing and treating patients with this condition.
Topics & Concepts
EtiologyDiseaseImmune systemMedicineRare diseaseIntensive care medicineImmunologyPathologyIgG4-Related and Inflammatory DiseasesNeuroendocrine Tumor Research AdvancesSoft tissue tumor case studies