Nervonic Acid Attenuates Accumulation of Very Long-Chain Fatty Acids and is a Potential Therapy for Adrenoleukodystrophy
Márcia R. Terluk, Julianne Tieu, Siddhee A. Sahasrabudhe, Ann B. Moser, Paul A. Watkins, Gerald V. Raymond, Reena V. Kartha
Topics & Concepts
AdrenoleukodystrophyNeurologyChemistryFatty acidLipidologyChain (unit)Internal medicineEndocrinologyMedicineBiochemistryNeurosciencePsychologyPeroxisomePhysicsGeneAstronomyPeroxisome Proliferator-Activated ReceptorsSphingolipid Metabolism and SignalingAdipose Tissue and Metabolism