Litcius/Paper detail

Multisystem Inflammatory Syndrome in Children (MIS-C), a Post-viral Myocarditis and Systemic Vasculitis—A Critical Review of Its Pathogenesis and Treatment

Jeremy C. McMurray, Joseph W. May, Madeleine W. Cunningham, Olcay Y. Jones

2020Frontiers in Pediatrics175 citationsDOIOpen Access PDF

Abstract

MIS-C is a newly defined post-viral myocarditis and inflammatory vasculopathy of children following COVID-19 infection. This review summarizes the literature on diagnosis, parameters of disease severity, and current treatment regimens. The clinical perspective was analyzed in light of potential immunopathogenesis and compared to other post-infectious and inflammatory illnesses of children affecting the heart. In this paradigm, the evidence supports the importance of endothelial injury and activation of the IL-1 pathway as a common determinant among MIS-C, Kawasaki disease, and Acute Rheumatic fever.

Topics & Concepts

MedicineKawasaki diseasePathogenesisMyocarditisViral MyocarditisVasculitisImmunologyDiseaseSystemic vasculitisPathologyInternal medicineArteryKawasaki Disease and Coronary ComplicationsInflammasome and immune disordersMechanical Circulatory Support Devices