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PSCs Reveal PUFA-Provoked Mitochondrial Stress as a Central Node Potentiating RPE Degeneration in Bietti’s Crystalline Dystrophy

Zhao Zhang, Bin Yan, Fei Gao, Qing Li, Xiaohong Meng, Peikai Chen, Lei Zhou, Wen Deng, Cheng Li, Weiyi Xu, Shuo Han, Feng Hong, Yaping Li, Junhui Chen, Zhengqin Yin, Can Liao, Hung‐Fat Tse, Xu Aimin, Qizhou Lian

2020Molecular Therapy41 citationsDOIOpen Access PDF

Topics & Concepts

Degeneration (medical)Oxidative stressDystrophyBiologyCell biologyGeneticsMedicineOphthalmologyEndocrinologyMitochondrial Function and PathologyGenetic Neurodegenerative DiseasesRNA regulation and disease
PSCs Reveal PUFA-Provoked Mitochondrial Stress as a Central Node Potentiating RPE Degeneration in Bietti’s Crystalline Dystrophy | Litcius