Fibroblast-Secreted Phosphoprotein 1 Mediates Extracellular Matrix Deposition and Inhibits Smooth Muscle Cell Contractility in Marfan Syndrome Aortic Aneurysm
Mei Zhou, Yuexin Zhu, Zeyi Zhou, Feiran Qi, Shuai Zheng, Shijuan Gao, Yulin Li, Yan Liu, Jie Du
Topics & Concepts
Extracellular matrixFibroblastThoracic aortic aneurysmPeriostinLysyl oxidaseMarfan syndromeCell biologyBiologyAortic aneurysmImmunostainingInternal medicineImmunologyMedicineCell cultureAortaImmunohistochemistryGeneticsConnective tissue disorders researchAortic aneurysm repair treatmentsAortic Disease and Treatment Approaches