The attenuated hepatic clearance of propionate increases cardiac oxidative stress in propionic acidemia
You Wang, Suhong Zhu, Wentao He, Hannah Marchuk, Eva Richard, Lourdes R. Desviat, Sarah P. Young, Dwight D. Koeberl, Takhar Kasumov, Xiaoxin Chen, Guofang Zhang
Topics & Concepts
Propionic acidemiaPropionateOxidative stressInternal medicineMedicineOxidative phosphorylationEndocrinologyChemistryCardiologyBiochemistryMetabolism and Genetic DisordersDiet and metabolism studiesLiver Disease Diagnosis and Treatment