Givinostat as metabolic enhancer reverting mitochondrial biogenesis deficit in Duchenne Muscular Dystrophy
Matteo Giovarelli, Silvia Zecchini, Giorgia Catarinella, Claudia Moscheni, Patrizia Sartori, C. Barbieri, Paulina Roux-Biejat, Alessandra Napoli, Chiara Vantaggiato, Davide Cervia, Cristiana Perrotta, Emilio Clementi, Lucia Latella, Clara De Palma
Topics & Concepts
Mitochondrial biogenesisMitochondrionBiologyDuchenne muscular dystrophyMuscular dystrophyMitochondrial diseaseDystrophinMitochondrial myopathyCell biologyUtrophinMitochondrial DNAGeneticsGeneMuscle Physiology and DisordersMitochondrial Function and PathologyAdipose Tissue and Metabolism