FLCN-Driven Functional Adrenal Cortical Carcinoma with High Mitotic Tumor Grade: Extending the Endocrine Manifestations of Birt-Hogg-Dubé Syndrome
Renee Hofstedter, María Carolina Sanabria‐Salas, Di Jiang, Shereen Ezzat, Özgür Mete, Raymond H. Kim
Topics & Concepts
FolliculinBirt–Hogg–Dubé syndromeLoss of heterozygosityGermlineAdrenocortical carcinomaMedicineMalignancyPathologyMultiple endocrine neoplasiaAdrenal glandGermline mutationCancer researchInternal medicineBiologyAllelePneumothoraxGeneticsMutationGeneAnatomyRenal cell carcinoma treatmentAdrenal and Paraganglionic TumorsMicrotubule and mitosis dynamics