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Hemophagocytic lymphohistiocytosis during pregnancy: a review of the literature in epidemiology, pathogenesis, diagnosis and treatment

Lidong Liu, Yutong Cui, Qiongjie Zhou, Huanqiang Zhao, Xiaotian Li

2021Orphanet Journal of Rare Diseases24 citationsDOIOpen Access PDF

Abstract

Hemophagocytic lymphohistiocytosis during pregnancy is rare; it is often misdiagnosed, resulting in a high maternal and foetal mortality rate. Herein, based on limited case reports including antepartum and postpartum cases, we reviewed the current studies of pregnancy-related hemophagocytic lymphohistiocytosis, and compared the epidemiology, aetiology, diagnosis and treatment of pregnancy-related hemophagocytic lymphohistiocytosis with non-pregnancy, enriching the understanding of hemophagocytic lymphohistiocytosis and its treatment in obstetrics.

Topics & Concepts

Hemophagocytic lymphohistiocytosisPregnancyMedicineEtiologyEpidemiologyIntensive care medicinePediatricsObstetricsImmunologyDiseaseInternal medicineBiologyGeneticsAutoimmune and Inflammatory Disorders ResearchAdolescent and Pediatric HealthcareParvovirus B19 Infection Studies