Imaging brain glucose metabolism in vivo reveals propionate as a major anaplerotic substrate in pyruvate dehydrogenase deficiency
Isaac Marin‐Valencia, Arif Kocabas, Carlos Rodríguez‐Navas, Vesselin Z. Miloushev, Manuel González-Rodríguez, Hannah Lees, Kelly E. Henry, Jake Vaynshteyn, Valerie A. Longo, Kofi Deh, Roozbeh Eskandari, Arsen Mamakhanyan, Marjan Berishaj, Kayvan R. Keshari
Topics & Concepts
Pyruvate dehydrogenase complexPropionateBiochemistryIn vivoGlycolysisBiologyMetabolismMitochondrionEnzymeBiotechnologyDiet and metabolism studiesMitochondrial Function and PathologyMetabolism and Genetic Disorders