Litcius/Paper detail

Confirming the involvement of <scp><i>PIEZO2</i></scp> in the etiology of <scp>Marden–Walker</scp> syndrome

Mohammed Zain Seidahmed, Sateesh Maddirevula, Abeer M. Miqdad, Abdullah Al Faifi, Abdulmohsen Al Samadi, Fowzan S. Alkuraya

2020American Journal of Medical Genetics Part A11 citationsDOI

Abstract

Pathogenic heterozygous variants in PIEZO2 typically cause distal arthrogryposis type 5 (DA5) and the closely related Gordon syndrome (GS). Only one case of PIEZO2-related Marden-Walker syndrome (MWS) has been reported to date. We report the phenotypic features of a Saudi female patient with features consistent with MWS in whom we identified a novel de novo likely pathogenic variant in PIEZO2. Our case lends support to the link between PIEZO2 and MWS.

Topics & Concepts

EtiologyMedicineInternal medicineErythrocyte Function and PathophysiologyHemoglobinopathies and Related DisordersFetal and Pediatric Neurological Disorders