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Upper motor neurons are a target for gene therapy and UCHL1 is necessary and sufficient to improve cellular integrity of diseased upper motor neurons

Barış Genç, Javier H. Jara, Santana S. Sanchez, Amiko K. B. Lagrimas, Öge Gözütok, Nuran Koçak, Yongling Zhu, P. Hande Özdi̇nler

2021Gene Therapy20 citationsDOIOpen Access PDF

Topics & Concepts

Amyotrophic lateral sclerosisNeurodegenerationMotor neuronBiologyNeuroscienceSOD1Hereditary spastic paraplegiaUpper motor neuronDeubiquitinating enzymeGenetic enhancementUbiquitinSpinal cordCell biologyGeneDiseasePathologyMedicineGeneticsPhenotypeAmyotrophic Lateral Sclerosis ResearchNeurogenetic and Muscular Disorders ResearchNerve injury and regeneration
Upper motor neurons are a target for gene therapy and UCHL1 is necessary and sufficient to improve cellular integrity of diseased upper motor neurons | Litcius