CT Honeycombing and Traction Bronchiectasis Extent Independently Predict Survival across Fibrotic Interstitial Lung Disease Subtypes
Daniel-Costin Marinescu, Cameron Hague, Néstor L. Müller, Darra Murphy, Andrew Churg, Joanne L Wright, A. Al-Arnawoot, Ana-Maria Bilawich, Patrick Bourgouin, Gerard Cox, C. Durand, T. Elliot, Jennifer Ellis, Jolene H. Fisher, D. Fladeland, Amanda Grant-Orser, G.C. Goobie, Z. Guenther, Ehsan Haider, Nathan Hambly, James Huynh, Kerri A. Johannson, Geoffrey Karjala, Nasreen Khalil, Martin Kolb, Lauren Lapointe‐Shaw, Jonathon Leipsic, S.D. Lok, S. Macisaac, Micheal McInnis, H. Manganas, Veronica Marcoux, John R. Mayo, Julie Morisset, Ciaran Scallan, T. Sedlic, Shane Shapera, Kelly Sun, V. Tan, Alyson W. Wong, Boyang Zheng, Christopher J. Ryerson
Abstract
Extent of fibrosis, defined by the amount of honeycombing and traction bronchiectasis, was consistently associated with death or lung transplant across all interstitial lung disease subtypes in a dose-dependent fashion.