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Aggregation of mutant cysteine string protein-α via Fe–S cluster binding is mitigated by iron chelators

Nima Naseri, Burçe Ergel, Parinati Kharel, Yoonmi Na, Qingqiu Huang, Rong Huang, Natalia Dolzhanskaya, Jacqueline Burré, Milen Velinov, Manu Sharma

2020Nature Structural & Molecular Biology21 citationsDOIOpen Access PDF

Topics & Concepts

MutantCysteineCell biologyChemistryNeuronal ceroid lipofuscinosisMutationProtein aggregationBiochemistryBiologyGeneEnzymeLysosomal Storage Disorders ResearchCellular transport and secretionRNA regulation and disease
Aggregation of mutant cysteine string protein-α via Fe–S cluster binding is mitigated by iron chelators | Litcius