Litcius/Paper detail

Efficacy and safety of ataluren in patients with nonsense-mutation cystic fibrosis not receiving chronic inhaled aminoglycosides: The international, randomized, double-blind, placebo-controlled Ataluren Confirmatory Trial in Cystic Fibrosis (ACT CF)

Michael W. Konstan, Donald R. VanDevanter, Steven M. Rowe, M. Wilschanski, Eitan Kerem, Isabelle Sermet‐Gaudelus, Emily DiMango, Paola Melotti, Joseph McIntosh, K. De Boeck

2020Journal of Cystic Fibrosis66 citationsDOIOpen Access PDF

Topics & Concepts

MedicineCystic fibrosisPlaceboInternal medicineRandomized controlled trialNonsense mutationPediatricsMutationPathologyAlternative medicineMissense mutationGeneticsBiologyGeneCystic Fibrosis Research AdvancesRespiratory viral infections researchBiological Research and Disease Studies