Short-term effect of elexacaftor-tezacaftor-ivacaftor on lung function and transplant planning in cystic fibrosis patients with advanced lung disease
B Bermingham, A. Rueschhoff, G. Ratti, A Nesmith, Dana L. Goodwin, S. Gray, Patrick A. Flume, Solomon G. M, Limor Cohen, Bryan Garcia
Topics & Concepts
IvacaftorMedicineCystic fibrosisLung transplantationLung functionLungInternal medicineStage (stratigraphy)Lung diseaseDiseaseIntensive care medicineCystic fibrosis transmembrane conductance regulatorBiologyPaleontologyCystic Fibrosis Research AdvancesTracheal and airway disordersPneumocystis jirovecii pneumonia detection and treatment