Nutritional co-therapy with 1,3-butanediol and multi-ingredient antioxidants enhances autophagic clearance in Pompe disease
Mats I. Nilsson, Michael Crozier, Alessia Di Carlo, Donald Xhuti, Katherine Manta, Liza J. Roik, Adam L. Bujak, Joshua P. Nederveen, Milla G. Tarnopolsky, Bart P. Hettinga, Naresh Kumar Meena, Nina Raben, Mark A. Tarnopolsky, Mark A. Tarnopolsky, Mark A. Tarnopolsky
Topics & Concepts
Ketone bodiesAutophagyIngredientKetogenic dietOxidative stressEnzyme replacement therapyPharmacologyMedicineSkeletal muscleAntioxidantKetosisFlux (metallurgy)ChemistryAdjunctive treatmentCreatineInternal medicineBiochemistryEndocrinologyDiseaseMetabolismPathologyApoptosisDiabetes mellitusEpilepsyPsychiatryOrganic chemistryDiet and metabolism studiesLysosomal Storage Disorders ResearchGlycogen Storage Diseases and Myoclonus