Nucleolar disruption, activation of P53 and premature senescence in POLR3A-mutated Wiedemann-Rautenstrauch syndrome fibroblasts

Cindy Tatiana Báez-Becerra, Estefania Valencia-Rincón, Karen L. Velásquez-Méndez, Nelson J. Ramírez-Suárez, Claudia Guevara, Adrián G. Sandoval‐Hernández, Carlos Bustos, Leonora Olivos-Cisneros, Gabriel Gutiérrez‐Ospina, Humberto Arboleda, Gonzálo Arboleda