Litcius/Paper detail

PUS7 deficiency in human patients causes profound neurodevelopmental phenotype by dysregulating protein translation

Sangwoo T. Han, Andrew C. Kim, Karolyn Garcia, Lisa A. Schimmenti, Ellen F. Macnamara, Undiagnosed Diseases Network, William A. Gahl, May Christine V. Malicdan, Cynthia J. Tifft

2022Molecular Genetics and Metabolism21 citationsDOIOpen Access PDF

Topics & Concepts

Autism spectrum disorderTranslation (biology)PhenotypeDownregulation and upregulationAutismProbandGeneBiologyProtein biosynthesisNeurodevelopmental disorderGeneticsMedicineMessenger RNAMutationPsychiatryBiochemical and Molecular ResearchCytomegalovirus and herpesvirus researchRNA modifications and cancer