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Primary Aortic Angiosarcoma: A Review of Two Cases Highlighting Unique Imaging and Clinical Characteristics

Case Keltner, Ana Paula Santos Lima, Malinda West, Kenneth R. Gundle, Cristina Fuss, Lara E. Davis

2021Radiology Cardiothoracic Imaging12 citationsDOIOpen Access PDF

Abstract

Angiosarcomas are rare vascular connective tissue tumors originating from the tunica intima, media, or adventitia and may arise in large vessels. Here two cases of primary angiosarcoma of the aorta are described that highlight initial manifestations and unique complications from diffuse arterial tumor emboli, which led to delayed cancer diagnosis. In patients with aortic lesions, imaging characteristics must be thoughtfully reconciled with clinical scenarios, particularly in patients with no additional evidence of atherosclerosis or vasculitis. Keywords: Oncology, Neoplasms-Primary, MR-Angiography, Aorta © RSNA, 2021

Topics & Concepts

MedicineAngiosarcomaTunica mediaAortaRadiologyVasculitisPathologyAngiographyConnective tissueInternal medicineCarotid arteriesDiseaseCardiac tumors and thrombiVascular Tumors and AngiosarcomasSarcoma Diagnosis and Treatment
Primary Aortic Angiosarcoma: A Review of Two Cases Highlighting Unique Imaging and Clinical Characteristics | Litcius