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Normalisation of circulating neutrophil counts after 12 months of elexacaftor-tezacaftor-ivacaftor in patients with advanced cystic fibrosis

Théo Dhôte, Clémence Martin, Lucile Regard, Lucie Pesenti, Reem Kanaan, Nicolas Carlier, Isabelle Honoré, Jennifer Da Silva, Véronique Witko‐Sarsat, Pierre‐Régis Burgel

2022European Respiratory Journal20 citationsDOI

Abstract

<b>In people with cystic fibrosis and advanced lung disease, circulating neutrophils were often elevated under clinically stable conditions. Treatment with elexacaftor-tezacaftor-ivacaftor for 12 months is associated with normalisation of neutrophil counts.</b> http://bit.ly/3gtgDFx

Topics & Concepts

IvacaftorCystic fibrosisMedicineInternal medicineDiseaseGastroenterologyPathologyCystic fibrosis transmembrane conductance regulatorCystic Fibrosis Research AdvancesTracheal and airway disordersNeonatal Respiratory Health Research
Normalisation of circulating neutrophil counts after 12 months of elexacaftor-tezacaftor-ivacaftor in patients with advanced cystic fibrosis | Litcius