Disturbance of bioenergetics and calcium homeostasis provoked by metabolites accumulating in propionic acidemia in heart mitochondria of developing rats
Ana Cristina Roginski, Alessandro Wajner, Cristiane Cecatto, Simone Magagnin Wajner, Roger F. Castilho, Moaçir Wajner, Alexandre Umpierrez Amaral
Topics & Concepts
MitochondrionPyruvate dehydrogenase complexInternal medicineCarnitineEndocrinologyMitochondrial permeability transition poreBioenergeticsHomeostasisRespirationBiochemistryBiologyCalciumChemistryMedicineEnzymeProgrammed cell deathBotanyApoptosisMitochondrial Function and PathologyMetabolism and Genetic DisordersGenetic Neurodegenerative Diseases