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Effects of Enzyme Replacement Therapy on Cardiac MRI Findings in Fabry Disease: A Systematic Review and Meta-Analysis

Stefano Figliozzi, Eleni Kollia, Alexandros Simistiras, Antonia Camporeale, Kamil Stankowski, Pier Giorgio Masci, George Mavraganis, Massimo Lombardi, Gianluigi Condorelli, Marco Francone, Maurizio Pieroni, Georgios Georgiopoulos

2024Radiology Cardiothoracic Imaging13 citationsDOIOpen Access PDF

Abstract

To perform a systematic review and meta-analysis to assess the effect of enzyme replacement therapy on cardiac MRI parameters in patients with Fabry disease.

Topics & Concepts

Enzyme replacement therapyFabry diseaseMeta-analysisMedicineDiseaseInternal medicineCardiologyLysosomal Storage Disorders ResearchGlycogen Storage Diseases and MyoclonusStudies on Chitinases and Chitosanases
Effects of Enzyme Replacement Therapy on Cardiac MRI Findings in Fabry Disease: A Systematic Review and Meta-Analysis | Litcius