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Regional metabolic signatures in the Ndufs4(KO) mouse brain implicate defective glutamate/α-ketoglutarate metabolism in mitochondrial disease

Simon C. Johnson, Ernst‐Bernhard Kayser, Rebecca Bornstein, Julia Stokes, Alessandro Bitto, Kyung Yeon Park, Amanda Pan, Grace X Sun, Daniel Raftery, Matt Kaeberlein, Margaret M. Sedensky, Philip G. Morgan

2020Molecular Genetics and Metabolism49 citationsDOIOpen Access PDF

Topics & Concepts

BiologyGlutamatergicNeurodegenerationGlutamate receptorPI3K/AKT/mTOR pathwayKnockout mouseGlutamineMitochondrionCitric acid cycleCell biologyMetabolismBiochemistryInternal medicineSignal transductionMedicineAmino acidDiseaseReceptorMitochondrial Function and PathologyATP Synthase and ATPases ResearchMetabolism and Genetic Disorders
Regional metabolic signatures in the Ndufs4(KO) mouse brain implicate defective glutamate/α-ketoglutarate metabolism in mitochondrial disease | Litcius