Cystic fibrosis-related liver disease: Clinical presentations, diagnostic and monitoring approaches in the era of CFTR modulator therapies
Jérémy Dana, Dominique Debray, Aurélie Bèaufrere, Sophie Hillaire, Monique Fabrè, Caroline Reinhold, Thomas F. Baumert, Laureline Berteloot, Valérie Vilgrain
Topics & Concepts
MedicineCystic fibrosisLiver transplantationCirrhosisLiver diseasePortal hypertensionAsymptomaticBiliary cirrhosisPathologyBiliary atresiaInternal medicineGastroenterologyDiseaseTransplantationAutoimmune diseaseCystic Fibrosis Research AdvancesGenetic and Kidney Cyst DiseasesPediatric Hepatobiliary Diseases and Treatments