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ASPM promotes homologous recombination-mediated DNA repair by safeguarding BRCA1 stability

Shibin Xu, Xingxuan Wu, Peipei Wang, Sheng‐Li Cao, Bin Peng, Xingzhi Xu

2021iScience38 citationsDOIOpen Access PDF

Abstract

) gene encodes a spindle protein that is commonly implicated in primary microcephaly. We found that ASPM is recruited to sites of DNA damage in a PARP2-dependent manner. ASPM interacts with BRCA1 and its E3 ligase HERC2, preventing HERC2 from accessing to BRCA1 and ensuring BRCA1 stability. Inhibition of ASPM expression promotes HERC2-mediated BRCA1 degradation, compromises HR repair efficiency and chromosome stability, and sensitizes cancer cells to ionizing radiation. Moreover, we observed a synergistic effect between ASPM and PARP inhibition in killing cancer cells. This research has uncovered a novel function for ASPM in facilitating HR-mediated repair of DSBs by ensuring BRCA1 stability. ASPM might constitute a promising target for synthetic lethality-based cancer therapy.

Topics & Concepts

Homologous recombinationSafeguardingDNA repairDNAHomologous chromosomeBiologyComputational biologyGeneticsChemistryCell biologyMedicineGeneNursingCRISPR and Genetic EngineeringDNA Repair MechanismsPARP inhibition in cancer therapy
ASPM promotes homologous recombination-mediated DNA repair by safeguarding BRCA1 stability | Litcius