Granulomatosis With Polyangiitis (Wegener's Granulomatosis) Complicated by Pericarditis: Our Experience of Two Cases and Comparative Review of Literature
Taha Ahmed, Dane Meredith, Allan L. Klein
Abstract
•GPA is a systemic necrotizing vasculitis of medium and small vessels.•GPA classically involves the upper and lower respiratory tracts and the kidneys.•Pericarditis is a common cardiac manifestation, but RP is rarely described.•A systematic literature search yielded 13 cases of acute pericarditis secondary to GPA, which are analyzed in this review.•The potential role of Anakinra for debilitating RP secondary to GPA is described.
Topics & Concepts
Granulomatosis with polyangiitisMedicinePericarditisNecrotizing VasculitisVasculitisAnakinraWegener granulomatosisDermatologyCardiologyPathologyInternal medicineDiseaseVasculitis and related conditionsSarcoidosis and Beryllium Toxicity ResearchPericarditis and Cardiac Tamponade