Unfolding the pathophysiology of congenital thrombotic thrombocytopenic purpura in pregnancy: lessons from a cluster of familial cases
Shayna Miodownik, Oleg Pikovsky, Offer Erez, Yarden Kezerle, Oleg Lavon, Anat Rabinovich
Topics & Concepts
MedicineADAMTS13Thrombotic thrombocytopenic purpuraPregnancyPreeclampsiaThrombotic microangiopathyVon Willebrand factorCohortPremature rupture of membranesPediatricsObstetricsConsanguinityInternal medicineFetusPlateletDiseaseBiologyGeneticsComplement system in diseasesCoagulation, Bradykinin, Polyphosphates, and AngioedemaBlood Coagulation and Thrombosis Mechanisms