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Evaluation of age at symptom onset, proband status, and sex as predictors of disease severity in pediatric catecholaminergic polymorphic ventricular tachycardia

Dania Kallas, Thomas M. Roston, Sonia Franciosi, Laura Brett, Krystien V.V. Lieve, Sit‐Yee Kwok, Prince J. Kannankeril, Andrew D. Krahn, Martin J. LaPage, Susan P. Etheridge, Allison C. Hill, Christopher L. Johnsrude, James C. Perry, Linda Knight, Peter Fischbach, Seshadri Balaji, Svjetlana Tisma‐Dupanovic, Ian H. Law, Joseph Atallah, David Backhoff, Anna Kamp, Peter Kubuš, Adam C. Kean, Peter F. Aziz, Joshua Kovach, Yung R. Lau, Jordana Kron, Sally-Ann B. Clur, Georgia Sarquella‐Brugada, Arthur A.M. Wilde, Shubhayan Sanatani

2021Heart Rhythm28 citationsDOIOpen Access PDF

Topics & Concepts

MedicineProbandCatecholaminergic polymorphic ventricular tachycardiaInternal medicineCardiologyDiseaseTachycardiaAge of onsetPediatricsMutationRyanodine receptorChemistryRyanodine receptor 2CalciumBiochemistryGeneCardiac electrophysiology and arrhythmiasCardiac Arrhythmias and TreatmentsAtrial Fibrillation Management and Outcomes
Evaluation of age at symptom onset, proband status, and sex as predictors of disease severity in pediatric catecholaminergic polymorphic ventricular tachycardia | Litcius