Predictors of acute metabolic decompensation in children with maple syrup urine disease at the emergency department
Yılmaz Yıldız, Leman Akcan Yıldız, Ali Dursun, Ayşegül Tokatlı, Turgay Coşkun, Özlem Tekşam, Sivri Hs
Topics & Concepts
Maple syrup urine diseaseMedicineEmergency departmentDecompensationUrineDiseaseIntensive care medicinePediatricsEmergency medicineInternal medicineAmino acidLeucineBiochemistryChemistryPsychiatryMetabolism and Genetic DisordersDiabetes and associated disordersLiver Disease Diagnosis and Treatment