Elevated plasma β-hydroxybutyrate predicts adverse outcomes and disease progression in patients with arrhythmogenic cardiomyopathy
Jiangping Song, Liang Chen, Xiao Chen, Jie Ren, Ningning Zhang, Tiara Tirasawasdichai, Zhenliang Hu, Wei Hua, Yiran Hu, Huiru Tang, Huei-Sheng Vincent Chen, Sheng-Shou Hu
Abstract
< 0.001). Among 94 relatives of probands, higher plasma β-OHB distinguished 25 relatives having suspected AC from nonaffected relatives. This study demonstrates that elevated plasma β-OHB predicts MACE in probands and disease progression in patients with AC and their clinically asymptomatic relatives.
Topics & Concepts
MedicineCardiomyopathyAdverse effectInternal medicineDiseaseCardiologyHeart failureCardiovascular Effects of ExerciseCardiac Imaging and DiagnosticsCardiac Arrest and Resuscitation