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Ivacaftor improves lung disease in patients with advanced CF carrying CFTR mutations that confer residual function

Donatello Salvatore, Vito Terlizzi, Michela Francalanci, Giovanni Taccetti, Barbara Messore, Carlotta Biglia, Giovanna Pisi, Maria Adelaide Calderazzo, Mimma Caloiero, Giovanna Pizzamiglio, Fabio Majo, Federico Cresta, Giuseppina Leonetti, Domenica De Venuto

2020Respiratory Medicine29 citationsDOI

Topics & Concepts

IvacaftorMedicineCystic fibrosisInternal medicineGastroenterologyPulmonary function testingAdverse effectCystic fibrosis transmembrane conductance regulatorCystic Fibrosis Research AdvancesNeonatal Respiratory Health ResearchPediatric health and respiratory diseases
Ivacaftor improves lung disease in patients with advanced CF carrying CFTR mutations that confer residual function | Litcius