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Anti‐inflammatory and immune‐mediated therapy for a case of febrile infection‐related epilepsy syndrome with rapid recurrence

Tomonori Kurimoto, Tsuyoshi Matsuoka, Yuki Ami, Koji Kanno, Takashi Fujii, Naoki Fujiwara, Takashi Matsuoka

2022Clinical Case Reports13 citationsDOIOpen Access PDF

Abstract

Febrile infection-related epilepsy syndrome (FIRES) is a disease of unknown etiology, characterized by refractory frequent focal seizures, which require prolonged intensive care. We successfully treated a boy with FIRES with anti-inflammatory and immunosuppressive therapy. This case suggests that an autoimmune mechanism may play a role in the development of FIRES.

Topics & Concepts

MedicineEtiologyEpilepsyRefractory (planetary science)DiseaseImmune systemEpilepsy syndromesIntensive care medicineImmunologyPediatricsInternal medicinePsychiatryPhysicsAstrobiologyInfectious Encephalopathies and EncephalitisEpilepsy research and treatmentBacterial Infections and Vaccines