Extracardiac Accumulation of Technetium-99m-Pyrophosphate in Transthyretin Cardiac Amyloidosis
Koji Takahashi, Daisuke Sasaki, Tomoki Sakaue, Daijiro Enomoto, Shigeki Uemura, Takafumi Okura, Shuntaro Ikeda, Daichi Yamamoto, Taizo Kono, Nobuhisa Yamamura
Abstract
This report presents a rare case of acute decompensated heart failure with technetium-99m-pyrophosphate accumulation in extracardiac sites, such as chest and abdominal walls, in addition to intense myocardial uptake of the tracer. Subsequently, an abdominal fat pad fine-needle aspiration biopsy, which provided positive findings for transthyretin amyloidosis, was performed. (Level of Difficulty: Advanced.)
Topics & Concepts
TransthyretinCardiac amyloidosisMedicinePyrophosphateAmyloidosisTechnetiumTechnetium-99mRadiologyBiopsyNuclear medicineInternal medicineScintigraphyChemistryBiochemistryEnzymeAmyloidosis: Diagnosis, Treatment, OutcomesParathyroid Disorders and TreatmentsMedical Imaging and Pathology Studies