Proteostatic imbalance and protein spreading in amyotrophic lateral sclerosis
M.E. Cicardi, Lara Marrone, Mimoun Azzouz, Davide Trotti
Topics & Concepts
Amyotrophic lateral sclerosisBiologyC9orf72SOD1Protein aggregationNeuroscienceInternalizationPathologicalExtracellularCell biologyDiseasePathologyGeneticsTrinucleotide repeat expansionCellMedicineGeneAlleleAmyotrophic Lateral Sclerosis ResearchPrion Diseases and Protein MisfoldingNeurological diseases and metabolism