Intravenous ketogenic diet therapy for neonatal-onset pyruvate dehydrogenase complex deficiency
Takehiko Inui, Yoichi Wada, Moriei Shibuya, Natsuko Arai‐Ichinoi, Yukimune Okubo, Wakaba Endo, Toshihiko Uchida, Noriko Togashi, Etsuo Naito, Kazuhiro Haginoya
Topics & Concepts
Ketogenic dietLactic acidosisMedicineEncephalopathyAcidosisInborn error of metabolismPediatricsMetabolic acidosisAtaxiaEpilepsyKetosisInternal medicineEndocrinologyDiabetes mellitusPsychiatryBiochemical Acid Research StudiesMitochondrial Function and PathologyMetabolism and Genetic Disorders