Longitudinal study of Pex1-G844D NMRI mouse model: A robust pre-clinical model for mild Zellweger spectrum disorder
Tanguy Demaret, Martin Roumain, Jérôme Ambroise, Jonathan Evraerts, Joachim Ravau, Caroline Bouzin, Bertrand Bearzatto, Jean‐Luc Gala, Hedwig Stepman, Sandrine Marie, Marie‐Françoise Vincent, Giulio G. Muccioli, Mustapha Najimi, Étienne Sokal
Topics & Concepts
Zellweger syndromeBiologyEndocrinologyInternal medicinePeroxisomal disorderPhenotypePeroxisomeGeneGeneticsMedicinePeroxisome Proliferator-Activated ReceptorsAdipose Tissue and MetabolismRNA Research and Splicing