Glycerophosphodiesters inhibit lysosomal phospholipid catabolism in Batten disease
Kwamina Nyame, Andy Hims, Aya Aburous, Nouf N. Laqtom, Wentao Dong, Uche N. Medoh, Julia C. Heiby, Jian Xiong, Alessandro Ori, Monther Abu-Remaileh
Topics & Concepts
BiologyLysosomeGlycerophospholipidBatten diseaseCatabolismCell biologyNeurodegenerationLysosomal storage diseaseAutophagyLipofuscinTransmembrane proteinBiochemistryTFEBPhospholipidEnzymeGeneMembraneDiseaseInternal medicineMedicineApoptosisReceptorLysosomal Storage Disorders ResearchCellular transport and secretionSphingolipid Metabolism and Signaling