A recessive variant in TFAM causes mtDNA depletion associated with primary ovarian insufficiency, seizures, intellectual disability and hearing loss
Farid Ullah, Waqar Rauf, Kamal Khan, Sheraz Khan, Katrina M. Bell, Vanessa Cristina de Oliveira Souza, Muhammad Tariq, Shabnam Bakhshalizadeh, Philippe Touraine, Nicholas Katsanis, Andrew Sinclair, Sijie He, Elena J. Tucker, Shahid Mahmood Baig, Erica E. Davis
Topics & Concepts
TFAMBiologyMitochondrial DNAGeneticsMitochondrial diseaseMitochondrionMitochondrial biogenesisPhenotypeCell biologyGeneMitochondrial Function and PathologyGenetic Neurodegenerative DiseasesDNA Repair Mechanisms