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Experience with ponatinib in paediatric patients with leukaemia

Jenna Rossoff, Van Huynh, Rachel E. Rau, Margaret E. Macy, Maria Luisa Sulis, Kirk R. Schultz, Michael J. Burke, Uma H. Athale, Maureen M. O’Brien, John Gregory, Inge M. van der Sluis, Frank G. Keller, C. Michel Zwaan, Meinolf Suttorp, Nobuko Hijiya

2020British Journal of Haematology35 citationsDOIOpen Access PDF

Abstract

Ponatinib has proven to be effective in adults with Philadelphia chromosome-positive leukaemias, but data in paediatrics are scarce. Among paediatric patients with chronic myeloid leukaemia (n = 9) or acute lymphoblastic leukaemia (n = 12) treated with varying doses of ponatinib in 13 centres, 71% showed a decrease in disease burden after a median of three months. Ponatinib was well tolerated, with grade 3 toxicities occurring in 29% of patients. Toxicities were similar to those reported in adults, with the exception of arterial thrombotic events, which were not observed. Ponatinib has a favourable safety profile in this paediatric cohort, but dose-finding studies are needed.

Topics & Concepts

PonatinibMedicineChronic myeloid leukaemiaPediatricsCohortLymphoblastic LeukemiaInternal medicineDiseaseLeukemiaMyeloid leukemiaDasatinibImatinibChronic Myeloid Leukemia TreatmentsAcute Lymphoblastic Leukemia researchChronic Lymphocytic Leukemia Research
Experience with ponatinib in paediatric patients with leukaemia | Litcius