Metabolic perturbations mediated by propionyl-CoA accumulation in organs of mouse model of propionic acidemia
Wentao He, You Wang, Erik J. Xie, Michael A. Barry, Guofang Zhang
Topics & Concepts
PropionateEndocrinologyInternal medicinePropionic acidemiaCarnitineMetabolismBiologyKetogenesisKetone bodiesChemistryMedicineBiochemistryMetabolism and Genetic DisordersMitochondrial Function and PathologyPeroxisome Proliferator-Activated Receptors