Litcius/Paper detail

A Genetics-First Approach Revealed Monogenic Disorders in Patients With ARM and VACTERL Anomalies

Romy van de Putte, Gabriel C. Dworschak, Erwin Brosens, Heiko Reutter, Carlo Marcelis, Rocío Acuña‐Hidalgo, Nehir Edibe Kurtas, Marloes Steehouwer, Sally L. Dunwoodie, Eberhard Schmiedeke, Stefanie Märzheuser, Nicole Schwarzer, Alice S. Brooks, Annelies de Klein, Cornelius E. J. Sloots, Dick Tibboel, Giulia Brisighelli, Anna Morandi, Maria Francesca Bedeschi, Michael D. Bates, Marc A. Levitt, Alberto Peña, Ivo de Blaauw, Nel Roeleveld, Han G. Brunner, Iris A.L.M. van Rooij, Alexander Hoischen

2020Frontiers in Pediatrics27 citationsDOIOpen Access PDF

Abstract

None of the other candidate genes were identified as novel unequivocal disease genes for VACTERL. However, a genetics-first approach allowed refinement of the clinical diagnosis in seven patients, in whom an alternative molecular-based diagnosis was found with important implications for the counseling of the families.

Topics & Concepts

MedicineLong armGeneticsMedical geneticsPediatricsChromosomeBiologyGeneEsophageal and GI PathologyTracheal and airway disordersCongenital Diaphragmatic Hernia Studies