A rare case report of granulomatosis with polyangiitis presenting with thrombus of the ascending aorta
Ioannis Tzanninis, Ahmed Elserwey, Alice Mason, John Rawlins
Abstract
Granulomatosis with polyangiitis (GPA) is a rare multisystem autoimmune antineutrophil cytoplasmic antibodies (ANCA) positive vasculitis that, in rare cases, can affect the aorta causing aortitis, aneurysm and rupture. A 50-year-old man presented with acute onset central chest pain, vomiting and
Topics & Concepts
MedicineGranulomatosis with polyangiitisAortitisAscending aortaVasculitisRare diseaseThrombusPancaAnti-neutrophil cytoplasmic antibodyChest painAortaRadiologyInternal medicineDiseaseVasculitis and related conditionsAtherosclerosis and Cardiovascular DiseasesRenal Diseases and Glomerulopathies