Litcius/Paper detail

Safety and efficacy of teclistamab in systemic immunoglobulin light chain amyloidosis

Rajshekhar Chakraborty, Divaya Bhutani, Mathew S. Maurer, Meera Mohan, Suzanne Lentzsch, Anita D’Souza

2023Blood Cancer Journal32 citationsDOIOpen Access PDF

Abstract

Bispecific antibodies (bsAbs) targeting B-cell maturation antigen (BCMA) have transformed the landscape of relapsed/refractory (R/R) multiple myeloma, with single-agent response rates of 60–70% in patients who have undergone extensive prior treatments [ 1 , 2 , 3 ]. To date, two BCMA-targeting bsAbs have received accelerated approval by the Food and Drug Administration in R/R myeloma-teclistamab and elranatamab. Immunoglobulin light chain (AL) amyloidosis is a related clonal plasma cell disorder, in which, one of the pillars of treatment is effective clone-directed therapy to rapidly achieve a deep hematologic response, ideally a very good partial response (VGPR) or better [ 4 , 5 ]. Traditionally, clone-directed therapies in AL amyloidosis have been borrowed from successful anti-myeloma therapies, with the most recent example being the anti-CD38 monoclonal antibody daratumumab [ 6 ]. Presently, the standard-of-care regimen for newly diagnosed AL amyloidosis is daratumumab in combination with cyclophosphamide-bortezomib-dexamethasone (Dara-CyBorD), which leads to a hematologic complete response (heme-CR) and ≥VGPR rate of about 50 and 80% respectively [ 6 ]. However, a critical unmet need remains in the management of patients who have suboptimal hematologic responses to Dara-CyBorD or experience relapse following this regimen. BCMA-targeting bsAbs are an enticing treatment option for AL amyloidosis due to several reasons: (a) they lead to rapid achievement of deep hematologic responses in myeloma, which is critical for achieving organ response in AL amyloidosis; (b) lower incidence of severe cytokine release syndrome (CRS) compared to other T-cell redirecting immunotherapies such as chimeric antigen receptor T-cell therapy. However, there are no prospective or retrospective studies documenting the safety and efficacy of teclistamab in patients with AL amyloidosis, who were excluded from the clinical trials in R/R myeloma. Here, we present data on seven consecutive patients with AL amyloidosis with or without concurrent R/R myeloma from two academic medical centers, who were treated with teclistamab since its FDA approval on 10/25/2022. The data cut-off for follow-up was 10/1/2023. De-identified clinical data can be shared with other investigators upon request to the corresponding author (R.C.).

Topics & Concepts

AmyloidosisImmunoglobulin light chainMedicineAntibodyImmunologyAL amyloidosisInternal medicineAmyloidosis: Diagnosis, Treatment, OutcomesMyeloproliferative Neoplasms: Diagnosis and TreatmentChronic Lymphocytic Leukemia Research