Improvement of the skeletal phenotype in a mouse model of diastrophic dysplasia after postnatal treatment with N-acetylcysteine
Chiara Paganini, Chiara Gramegna Tota, Luca Monti, Ilaria Monti, Antonio Maurizi, Mattia Capulli, Morgane Bourmaud, Anna Teti, Martine Cohen‐Solal, Simona Villani, Antonella Forlino, Andrea Superti‐Furga, Antonio Rossi
Topics & Concepts
Endochondral ossificationSulfationIntracellularCartilageEndocrinologyAcetylcysteineInternal medicineChemistryBiochemistryPhenotypeBiologyMedicineAnatomyGeneAntioxidantConnective tissue disorders researchBone health and treatmentsBone Metabolism and Diseases