Pkd1l1-deficiency drives biliary atresia through ciliary dysfunction in biliary epithelial cells
Yi Zou Lim, Min Zhu, Yunguan Wang, Tripti Sharma, Shannon Kelley, Estelle Oertling, Hao Zhu, Natasha Corbitt
Topics & Concepts
Biliary atresiaExtrahepatic Biliary AtresiaAlagille syndromeBiologyPathologyAtresiaInternal medicineFibrosisMedicineGastroenterologyCholestasisLiver transplantationTransplantationPediatric Hepatobiliary Diseases and TreatmentsDrug Transport and Resistance MechanismsCystic Fibrosis Research Advances