Dexamethasone-induced activation of heat shock response ameliorates seizure susceptibility and neuroinflammation in mouse models of Lafora disease
Priyanka Sinha, Bhupender Verma, Subramaniam Ganesh
Topics & Concepts
NeuroinflammationProteostasisLafora diseaseHSF1Progressive myoclonus epilepsyHeat shockBiologyHeat shock proteinNeuroscienceInternal medicineEndocrinologyEpilepsyMedicineCell biologyImmunologyHsp70InflammationGeneticsPhosphataseGenePhosphorylationGlycogen Storage Diseases and MyoclonusGenetics and Neurodevelopmental DisordersLysosomal Storage Disorders Research