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Autoimmune Pericarditis: Diagnosis and New Therapeutics

Heba Wassif, Elizabeth Ghandakly, Habib Layoun, Jaideep Singh Bhalla, Emily Littlejohn, Tom Kai Ming Wang, M. Elaine Husni, Allan Klein

2025Current Cardiology Reports7 citationsDOIOpen Access PDF

Abstract

PURPOSE OF REVIEW: To provide an overview of the diagnosis and updated therapeutic approach to autoimmune pericarditis. RECENT FINDINGS: Subtypes of autoimmune pericarditis may benefit from IL-1 inhibition and future phenotyping based on clinical presentation, biomarkers, and imaging may aid in guiding future therapeutic approaches. Autoimmune pericarditis is a unique phenotype of pericarditis for which there is scarce data. The clinical spectrum of pericardial involvement associated with autoimmune disorders varies in acuity, recurrence, severity, and symptomatic presentation. There is a pathophysiologic distinction that separates autoimmune and autoinflammatory pericarditis from other pericarditis presentations. This review explores the state of the art in diagnosis and therapeutic management.

Topics & Concepts

MedicinePericarditisAcute pericarditisPresentation (obstetrics)Therapeutic approachIntensive care medicineDermatologyPathologyCardiologyDiseaseSurgeryPericarditis and Cardiac TamponadeMyasthenia Gravis and ThymomaTakotsubo Cardiomyopathy and Associated Phenomena
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